A RARE CASE OF ADRENAL GANGLIONEUROBLASTOMA WITH METASTASIZED LYMPH NODE IN A YOUNG ADULT

Nguyen Thao-Tram Le 1,, Tong Huong Diu 1, Nguyen Anh Viet 1, Bui Giang Van 2
1 Vinmec Nhatrang Hospital, Vinmec Health Care System
2 Vinmec Times City, Vinmec Health Care System

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Tóm tắt

Adrenal ganglioneuroblastoma is an extremely rare tumor among adrenal neoplasms in adult. We reported a 26-year-old young female patient presented with vague pain in left plank. Abdominal sonography and CTScan revealed a heterogenous solid lobulated left adrenal mass which contenting central necrosis, hemorrhage, coarse calcification and multiple adjacent metastasized lymphoid nodules, hence adrenal cortical carcinoma was not excluded although testing for adrenal function were normal. The patient was performed left adrenal surgery following by chemical therapy. Histiology was consistent with intermixed stroma-rich ganglioneuroblastoma. In literature, about 20 cases of adrenal ganglioneuroblastoma in adults were described, in which lymphoid metastasis was uncommon. Therefore, although adrenal ganglioneuroblastoma is obtained by histiology, imaging features should be invested further to differentiate from other neoplasms for appropriate treatment.  

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Tài liệu tham khảo

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