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Date Published: 02/12/2023
Abstract Views: 109
Views PDF: 63
DOI: https://doi.org/10.51298/vmj.v532i2.7386
Issue
Vol. 532 No. 2 (2023): Vietnam Medical Journal
Section
Các bài báo
How to Cite
Nguyen, T.-T. L. ., Tong, H. D. ., Nguyen, A. V. ., & Bui, G. V. . (2023). A RARE CASE OF ADRENAL GANGLIONEUROBLASTOMA WITH METASTASIZED LYMPH NODE IN A YOUNG ADULT. Vietnam Medical Journal, 532(2). https://doi.org/10.51298/vmj.v532i2.7386

A RARE CASE OF ADRENAL GANGLIONEUROBLASTOMA WITH METASTASIZED LYMPH NODE IN A YOUNG ADULT

Thao-Tram Le Nguyen1,, Huong Diu Tong1, Anh Viet Nguyen1, Giang Van Bui2
1 Vinmec Nhatrang Hospital, Vinmec Health Care System
2 Vinmec Times City, Vinmec Health Care System

Main Article Content

Abstract

Adrenal ganglioneuroblastoma is an extremely rare tumor among adrenal neoplasms in adult. We reported a 26-year-old young female patient presented with vague pain in left plank. Abdominal sonography and CTScan revealed a heterogenous solid lobulated left adrenal mass which contenting central necrosis, hemorrhage, coarse calcification and multiple adjacent metastasized lymphoid nodules, hence adrenal cortical carcinoma was not excluded although testing for adrenal function were normal. The patient was performed left adrenal surgery following by chemical therapy. Histiology was consistent with intermixed stroma-rich ganglioneuroblastoma. In literature, about 20 cases of adrenal ganglioneuroblastoma in adults were described, in which lymphoid metastasis was uncommon. Therefore, although adrenal ganglioneuroblastoma is obtained by histiology, imaging features should be invested further to differentiate from other neoplasms for appropriate treatment.  

Article Details

Keywords

Ganglioneuroblastoma in adult, ganglioneuroblastoma, neuroblastoma.

References

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