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Date Published: 20/12/2024
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DOI: https://doi.org/10.51298/vmj.v545i2.12309
Issue
Vol. 545 No. 2 (2024)
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Các bài báo
How to Cite
Nguyễn, B. T., Vũ, V. K., & Nguyễn, T. T. (2024). CASE REPORT: ACQURIED CENTRAL HYPOVENTILATION SYNDROME IN ADULT AFTER POSTERIOR FOSSA TUMOR RESECTION. Vietnam Medical Journal, 545(2). https://doi.org/10.51298/vmj.v545i2.12309

CASE REPORT: ACQURIED CENTRAL HYPOVENTILATION SYNDROME IN ADULT AFTER POSTERIOR FOSSA TUMOR RESECTION

Bá Tư Nguyễn, Văn Khâm Vũ, Toàn Thắng Nguyễn

Main Article Content

Abstract

Central hypoventilation syndrome (CHS) due to PHOX2B gene mutations in newborns causes a loss of automatic respiration. This condition is very rare in adults and can occur after posterior fossa surgeries near the respiratory center. This is a serious complication and can be fatal. We report a case of a 39-year-old man patient who was able to breathe normally on command but lost the automatic breathing reflex after microsurgical for tumor ressection in the fourth ventricle. The patient underwent tracheostomy and was treated with several respiratory stimulants but these interventions proved ineffective. The patient was then transferred to a primary local healthcare facility while remaining ventilator-dependent. This case highlights the significant challenges in prognostication, management, and treatment of patients with acquired CHS.

Article Details

Keywords

Ondine’s curse, central hypoventilation syndrome, brain tumor resection.

References

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