ĐÁNH GIÁ ĐẶC ĐIỂM LÂM SÀNG VÀ KẾT QUẢ ĐIỀU TRỊ HỘI CHỨNG CIANCIA

Abstract

Objective: This study was conducted to review the clinical characteristics and evaluate the results of treatment of Ciancia syndrome. Subjects and methods: Uncontrolled, descriptive intervention study on case series of patients diagnosed with Ciancia syndrome. Select a convenient sample size suitable to research criteria. Results: 9 patients with 18 eyes were included in this study. Strabismus symptom was detected between 1 and 5 months of age, with a mean age of onset of 2.9 months. Patients underwent surgical intervention had an average age of 13.8 months, the youngest is 9 months old, the oldest is 20 months old. All patients had mild hyperopia (from +1.00 D to +2.50 D) similar to children of the same age. The degree of strabismus ranges from +50 to +70 PD. The surgical method in all patients was to recess the medial rectus muscle in both eyes from 6.0 mm to 7.0 mm. 100% had good results in correcting ocular deviation after surgery, 88.9% had good results after a 6-month follow-up period. All patients had no limitation of ocular movements after surgery. During surgery, 5/9 patients had conjunctival hemorrhage. After surgery, 1/9 patients had a granulomatous reaction at the surgical edge. However, these complications were mild and resolved spontaneously during follow-up. Conclusion: Ciancia syndrome is a rare congenital internal strabismus syndrome, with large degree of strabismus, pseudo-restriction of extraocular movements, surgical treatment brings good results with low complications during and after surgery