MESO-REX SHUNT: A CASE RESPORT WITH COMPREHENSIVE DESCRIPTION OF SURGICAL PROCEDURE

Trí Trần Thanh, Duy Hồ Phi, Vi Trịnh Nguyễn Hạ, Kiệt Phan Tuấn, Thuận Lưu Nguyễn An, Trung Bùi Hải, Thiên Thân Trọng

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Abstract

Introduction: Extrahepatic portal vein obstruction (EHPVO) is a significant cause of portal hypertension in children. When the intrahepatic portal system remains intact, the Meso-Rex bypass is considered the standard treatment. In Vietnam, there are few reports on this condition, and no publications have detailed a comprehensive surgical technique. Patient and Methods: This report presents a successfully treated case using the Meso-Rex bypass. The diagnostic approach and surgical technique are described in detail. Results: A 7-year-old girl was admitted with hematemesis. Clinical examination revealed anemia and grade 3 splenomegaly. Laboratory results showed Hb 7.0 g/dL, platelet count 68,000/μL, and coagulopathy (PT 19.3s, INR 1.6). The patient was stabilized with somatostatin and packed red blood cell transfusion. Tests for protein C, protein S, and Factor V-Leiden were within normal limits. Contrast abdominal CT scan showed portal vein trunk thrombosis and cavernous transformation, with splenomegaly but no hepatic fibrosis or mass lesions. During a single anesthesia session, upper gastrointestinal endoscopy was performed (with variceal banding) and retrograde portography was conducted, confirming an intact intrahepatic portal system and a visible Rex. Meso-Rex shunt surgery was indicated and performed using the left internal jugular vein as a graft. Operative time was 270 minutes with an estimated blood loss of 50 ml. The shunt was patent and functional in the early postoperative period and remained satisfactory flow at 24-month follow-up, with velocities of 20–24 m/s. Conclusion: Retrograde portography is a crucial technique for evaluating the intrahepatic portal system and determining surgical eligibility for Meso-Rex bypass. Despite its technical complexity, the procedure restored physiological portal flow and yielded high treatment efficacy when properly indicated and performed.

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References

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