BÁO CÁO CA BỆNH HIẾM GẶP: CƠN BÃO THẬN TRÊN BỆNH NHÂN XƠ CỨNG BÌ (SCLERODERMA RENAL CRISIS)

Abstract

Scleroderma renal crisis (SRC) is a rare but potentially life-threatening complication of systemic sclerosis. The condition is characterized by severe hypertension, acute kidney injury, and thrombotic microangiopathy. Over the past decade, since the introduction of angiotensin-converting enzyme (ACE) inhibitors, both the incidence and mortality rates have declined; however, SRC remains a major clinical challenge due to the absence of effective preventive measures and its rapid progression, even when early intervention is initiated at the onset of renal involvement. We report a representative case recently managed at our center to highlight the critical importance of early recognition and prompt treatment of SRC in preventing irreversible renal damage.