CASE REPORT: MOYA MOYA DISEASE

Hoàng Đức Hạ1,2,, Trần Phan Ninh3, Nguyễn Thị Tuyết Nga4
1 Haiphong University of Medicine and Pharmacy
2 Hai Phong International General Hospital
3 Vietnam National Children's Hospital
4 Haiphong Children's Hospital

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Abstract

Case introduction: In this report, we introduced a case of a 12-year-old boy with clinical manifestations: sudden weakness in the left half of the body, no convulsions, no fever, no vomiting, and urinary incontinence. Computed tomography (CT) of the brain without contrast showed several foci of heterogeneous hypoattenuation in the right parietal subcortical white matter and bilateral periventricular white matter. Magnetic resonance imaging (MRI) with magnetic contrast injection showed an acute infarct in the right parietal lobe, several old cerebral infarctions in bilateral periventricular white matter, right occipital region and dynamic stenosis and bilateral internal carotid vessels due to Moyamoya disease. Conclusion: Moya Moya's pathology is a rare cerebrovascular disease, it should be suggested for children with recurrent headaches, unrelieved by conventional medications, and possibly accompanied by weakness in the limbs. CT scan or brain MRI or Digital subtraction angiography (DSA) helps to diagnose Moya Moya's disease, from which it is possible to plan an appropriate treatment for this disease.

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References

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