KHÍ PHẾ THŨNG THUỲ PHỔI BẨM SINH – TỔNG QUAN TÀI LIỆU VÀ BÁO CÁO CA BỆNH

Abstract

Congenital Lobar Emphysema (SLE) is known as congenital lobar hypertrophy, characterized by signs of increased size of the lobes. Most cases manifest within the first month of life; Symptoms of respiratory failure are typical. Mild cases are often missed and the disease may present in older children but is rare. Most cases of CLE involve partial or total obstruction of the bronchi, usually as a result of (a) bronchial cartilage defects; (b) extrinsic compression usually due to a vascular abnormality or a bronchial cyst, or (c) an abnormal bronchial mucosal fold. Some cases are not related to bronchial obstruction. CLE is most commonly located in the upper lobe of the left lung, followed by the upper and middle lobes of the right lung. Only a small percentage occurs in the lower lobe. Radiographs often show areas of luminosity or air trapping in the affected lobe. Mediastinal displacement is common due to abnormally distended lobes, and the normal lobes are hypovolemic. Surgical removal is necessary. We report a case of SLE detected in a 6-year-old child, located in the right middle and lower lobes. The patient had surgery to remove part of the right lower lobe after having the right pulmonary ventilation and perfusion assessment results, initially showing good treatment results.