IDIOPATHIC PULMONARY FIBROSIS - LITERATURE REVIEW AND CASE REPORT

Cung Văn Công1,
1 National Lung Hospital

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Abstract

Idiopathic Pulmonary Fibrosis (IPF) is the most common of the idiopathic interstitial lung diseases of unknown etiology. Its signs and symptoms are relatively nonspecific, and patients typically present with a chronic cough, progressive dyspnea, hypoxemia at rest or during exercise, and crackles on auscultation. Definitive diagnosis requires identification of common interstitial pneumonia (UIP) and exclusion of known causes of pulmonary fibrosis on High Resolution Computed Tomography (HRCT) of the chest or open lung biopsy. Multidisciplinary discussion (MDD) involving pulmonologists, radiologists, and pathologists with expertise in the diagnosis of IPF and other forms of interstitial lung disease is encouraged and often required. Management, treatment focused on antifibrotic therapy and early referral of patients to lung transplant centers are necessary. We introduce IPF case with full clinical, paraclinical, diagnostic and management procedures for your reference.

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References

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