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Date Published: 28/12/2022
Abstract Views: 166
Views PDF: 125
DOI: https://doi.org/10.51298/vmj.v520i1A.3787
Issue
Vol. 520 No. 1A (2022)
Section
Các bài báo
How to Cite
Anh Thơ, P. ., Thị Mỹ Thục, L. ., Chí Dũng, V. ., Thị Thúy Hồng, N. ., Văn Phú, P. ., Ngọc Khánh, N. ., & Thị Thanh Mai, Đỗ . (2022). ESTIMATION OF STATURE BASED ON TIBIAL LENGTH IN CHILDREN WITH POMPE DISEASE AT THE VIETNAMESE CHILDREN’S HOSPITAL. Vietnam Medical Journal, 520(1A). https://doi.org/10.51298/vmj.v520i1A.3787

ESTIMATION OF STATURE BASED ON TIBIAL LENGTH IN CHILDREN WITH POMPE DISEASE AT THE VIETNAMESE CHILDREN’S HOSPITAL

Phạm Anh Thơ1, Lưu Thị Mỹ Thục2, Vũ Chí Dũng2, Nguyễn Thị Thúy Hồng1,, Phạm Văn Phú1, Nguyễn Ngọc Khánh2, Đỗ Thị Thanh Mai2
1 Hanoi Medical University
2 Vietnam National Children's Hospital

Main Article Content

Abstract

Assessing nutritional status, especially stature measurement in children with Pompe disease is challenging due to delayed gross motor functions and/or musculoskeletal abnormalities. Objectives: To develop a predictive equation of stature in Pompe pediatric patients based on tibial length. Methods: 34 children with Pompe disease (1 – 82 months) at the Vietnamese Children’s Hospital were recruited, examined and measured to derive the equation for estimating stature based on tibial length. Results: The regression equation for estimating stature from tibial length was Ht = 3,29 x TL + 34,65 in children without musculoskeletal abnormalities and Ht = 3,29 x TL+33,95 in children with musculoskeletal abnormalities. After 3 months, the difference between actual and estimated stature was not statistically significant. Conclusion: Stature of children with Pompe disease can be estimated based on tibial length.

Article Details

Keywords

Pompe disease, nutritional assessment, estimated stature, tibial length, children

References

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