SIGNIFICANT FACIAL DEFORMITY WITH MULTIPLE DYSFUNCTIONS IN A PATIENT WITH A 15-YEAR-UNDIAGNOSED MELKERSSON-ROSENTHAL SYNDROME
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Abstract
Melkerrson-Rosenthal syndrome is a rare disorder of unknown aetiology and characterized by the triad of oro-facial edema, facial nerve palsy, and furrowing of the tongue. Two or more of the above are essential for making a clinical diagnosis. The mainstay of treatment is corticosteroids. Intralesional triamcinolone acetonide may be used for the treatment of oro-facial edema, along with oral ninocycline, doxycycline.
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References
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7. Basman A, Gumusok M, Degerli S, Kaya M, Toraman Alkurt M. Melkersson-rosenthal syndrome: a case report. J Istanb Univ Fac Dent 2017;51:42-45.
2. Rosenthal C. Klinisch-erbbiologischer Beitrag zur konstitutionspathologie. Zeitschrift für die gesamte Neurologie und Psychiatrie 1931;131:475-501.
3. Hornstein OP. Melkersson-Rosenthal syndrome. A neuro-muco-cutaneous disease of complex origin. Curr Probl Dermatol 1973;5:117-56.
4. Ziem PE, Pfrommer C, Goerdt S, Orfanos CE, Blume-Peytavi U. Melkersson-Rosenthal syndrome in childhood: a challenge in differential diagnosis and treatment. The British journal of dermatology 2000;143:860-3.
5. Desai SD, Dumraliya P, Mehta D. Melkersson-Rosenthal syndrome. J Neurosci Rural Pract 2014;5:S112-4.
6. Zimmer WM, Rogers RS, 3rd, Reeve CM, Sheridan PJ. Orofacial manifestations of Melkersson-Rosenthal syndrome. A study of 42 patients and review of 220 cases from the literature. Oral surgery, oral medicine, and oral pathology 1992;74:610-9.
7. Basman A, Gumusok M, Degerli S, Kaya M, Toraman Alkurt M. Melkersson-rosenthal syndrome: a case report. J Istanb Univ Fac Dent 2017;51:42-45.