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HEPATOPULMONARY SYNDROME IN CHILREN WITH CIRRHOSIS
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Abstract
Hepatopulmonary syndrome (HPS) is a rare complication. The rate appears from 4% - 40% in patients with cirrhosis. HPS is charactezied by the triad of chronic liver disease, abnormal arterial oxygenation congenital portosysmic shunts. HPS is considered a poor prognosis in cirrhotic patients. Supportive treatments pending a liver transplant include oxygen therapy, medications that help with pulmonary vasoconstriction, and some procedures such as TIPS. For the purposes of this article, we report a case of a 15-year-old female with cirrhosis of the liver with complications of portal hypertension with HPS syndrome. Diagnosis confirmed by transthoracic contrast echocardiography, contrast pulmonary angiography helps prognosis and reasonable treatment plan.
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Keywords
Hepatopulmonary syndrome, cirrhosis, transthoracic contrast echocardiography
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