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Date Published: 05/07/2023
Abstract Views: 361
Views PDF: 169
DOI: https://doi.org/10.51298/vmj.v527i2.5925
Issue
Vol. 527 No. 2 (2023)
Section
Các bài báo
How to Cite
Hoàng, H. Đức, Nguyễn, V. L., Ngô, T. T., Nguyễn, D. L., Nguyễn, L. B. T., & Võ, V. T. (2023). EPIDURAL HEMATOMA IN THALASSEMIA INTERMEDIA DUE TO EPIDURAL EXTRAMEDULLARY HEMATOPOIESIS: A CASE REPORT AND LITERATURE REVIEW. Vietnam Medical Journal, 527(2). https://doi.org/10.51298/vmj.v527i2.5925

EPIDURAL HEMATOMA IN THALASSEMIA INTERMEDIA DUE TO EPIDURAL EXTRAMEDULLARY HEMATOPOIESIS: A CASE REPORT AND LITERATURE REVIEW

Hữu Đức Hoàng1,, Viết Lực Nguyễn1, Thanh Tú Ngô1, Duy Linh Nguyễn1, Lê Bảo Tiến Nguyễn1, Văn Thanh Võ1,2
1 GERMANY FRIENDSHIP HOSPITAL
2 HMU

Main Article Content

Abstract

Epidural hematoma is a rare disease that can cause irreversible nerve damage if not treated promptly. Spinal cord epidural hematoma in Thalassemia intermedia patients is often caused by extramedullary hematopoiesis. The amount of blood produced in the patient's bone marrow is insufficient to supply the circulatory system. This extramedullary hematoma can cause spinal cord compression leading to clinical nerve damage: weakness, and paralysis. We report a case of a 15-year-old male patient diagnosed with Epidural Extramedullary Hematopoiesis in Beta -Thalassaemia T4-T8 level at the Department of Spine Surgery - Viet Duc University Hospital. An emergency T4-T7 decompressive laminectomy and blood transfusion were performed. One month postoperative, the patient has complete rehabilitation. Six months postoperative, there is no evidence of recurrence on MRI.

Article Details

Keywords

Spinal epidural hematoma, epidural hematoma, extramedullary hematopoiesis, Thalassemia intermedia,  -Thalassaemia

References

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