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Date Published: 18/09/2023
Abstract Views: 132
Views pdf: 69
DOI: https://doi.org/10.51298/vmj.v530i1.6644
Issue
Vol. 530 No. 1 (2023)
Section
Các bài báo
How to Cite
Ngô, T. T. H., Phạm, V. T., Diệp, Đình Được, Nguyễn, H. N., & Lâm, Q. T. (2023). PRIMARY PERICARDIAL SYNOVIAL SARCOMA: A RARE CASE REPORT AND LITERATURE REVIEW. Vietnam Medical Journal, 530(1). https://doi.org/10.51298/vmj.v530i1.6644

PRIMARY PERICARDIAL SYNOVIAL SARCOMA: A RARE CASE REPORT AND LITERATURE REVIEW

Thị Tuyết Hạnh Ngô1,2,3, Văn Tấn Phạm1,, Đình Được Diệp4, Hòa Nhơn Nguyễn4, Quốc Trung Lâm3
1 University of Medicine and Pharmacy at Ho Chi Minh City
2 Nguyen Tri Phuong hospital
3 Ho Chi Minh City University of Medicine and Pharmacy Hospital
4 Nguyen Tri Phuong Hospital

Main Article Content

Abstract

Pericardial synovinal sarcoma is a very rare disease that is difficult to diagnose and treat, and has a poor prognosis. We report a case of a 32-year-old man admitted to the hospital with exertional dyspnea for 3 months. Echocardiography, computed tomography, and chest magnetic resonance imaging revealed a pericardial tumor causing severe compression of the right ventricle, left atrium, and bilateral pulmonary veins, and narrowing the right ventricular outflow tract, with suspected invasion anterior to the right ventricular myocardium. The patient underwent partial resection of the tumor, which released the compression of the right ventricular outflow tract. The final pathological result was monophasic synovinal sarcoma. After surgery, the patient received chemotherapy, and follow-up after 5 months showed an improvement in clinical symptoms with no signs of the right ventricular outflow tract stenosis returning.

Article Details

Keywords

Synovial sarcoma, pericardial tumor.

References

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