GIÁN ĐOẠN ĐỘNG MẠCH PHỔI: BÁO CÁO LOẠT CA BỆNH

Abstract

Congenital discontinuous pulmonary artery (also known as unilateral absence of a pulmonary artery or absence of the proximal pulmonary artery) is a very rare lesion that is defined as complete absence of connection between the right and left pulmonary artery branches originating from the main pulmonary artery. If it is left untreated, this condition can lead to pulmonary artery hypoplasia and severe pulmonary hypertension in the lung where blood flow is supplied by the normally connected pulmonary artery. In this article, we report on a series of cases in newborns and infants with congenital discontinuous pulmonary arteries, where either one or both branches of the pulmonary arteries, both right and left, are supplied by blood from the patent ductus arteriosus in their same side. All patients underwent ductal stenting to keep the duct open and subsequently underwent surgical procedures to reestablish pulmonary artery circulation. Two patients experienced conditions of pulmonary hypertension and congestive heart failure immediately after the stent placement due to reperfusion. One patient experienced complete occlusion of the pulmonary artery connection two months after surgery, requiring the systemic to pulmonary shunt to ensure blood supply to the obstructed pulmonary artery before full repair could be performed. Congenital discontinuous pulmonary artery in children often does not have typical symptoms. The early intervention method of ductal stenting has proven to be effective. Additionally, cardiac intervention and surgery need to be closely coordinated in the treatment of the disease. Patients need to be intensively monitored to prevent complications."