RESULTS OF SURGICAL TREATMENT SACROCOCCYGEAL TERATOMA IN CHILDRENAT THE VIET NAM NATIONAL CHILDREN'S HOSPITAL

Thị Thủy Tiên Nguyễn, Duy Hiền Phạm , Xuân Nam Trần , Hồng Long Phan

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Abstract

Objective: sacrococcygeal teratoma (SCT) is an extragenital germ cell tumor originating from the coccyx, most of which are benign, but a few can be malignant or have the potential for malignancy. Early diagnosis and surgery are very important in the treatment and prognosis of the disease. The study aims to describe the clinical and pre-clinical characteristics of SCT and the operative outcomes of it. Methods: Retrospective study describing all patients diagnosed with sacrococcygeal teratoma, operated at the General Surgery Center of National Children's Hospital, from January 2016 to December 2022. Results: there were 44 patients including 14 male (31.8%) and 30 female (68.2%). The median age of patients was 44.5 days (2-4278 days). 41 patients (93.18%) had retrorectal surgery, 03 patients (6.82%) had combined abdominal and retrorectal surgery. The average operative time was 119 ± 37 minutes. Intraoperative complications: 08 patients (18.2%) bleeding due to damage to the anterior sacral plexus, stable blood transfusion; 01 patient (2.3%) perforated the posterior wall of the rectum, the puncture site was sutured, stable postoperatively, discharged after 17 days; 04 patients (9.09%) had ruptured tumor. Postoperative complications: 07 patients (15.91%) had surgical wound infection, 01 patient (2.27%) had bleeding from the surgical wound, which was sutured, 01 patient (2.27%) had urinary retention after surgery, and a catheter was placed. urinating and exercising reflexes to urinate, discharged after 25 days. No patient died during and after surgery. The mean hospital stay was 6.2 ± 4.5 days. Average follow-up time was 55.0 ± 23.8 months, 02 patients (6.5%) had bowel incontinence disorder, 03 patients (7.14%) had tumor recurrence and underwent tumor redo-resection. To date there has been no recurrence. Conclusions: Surgical treatment of Sacrococcygeal teratomain children can be performed safely and the recurrence rate is low.

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References

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