LAPAROSCOPIC SUGERY FOR BILATERAL PHEOCHROMOCYTOMA IN CHILDREN: A CASE REPORT

Duy Hiền Phạm , Mạnh Hoàn Vũ , Xuân Nam Trần , Hồng Long Phan , Thọ Anh Nguyễn, Hanh Tiệp Đặng , Chí Dũng Vũ , Thị Bích Ngọc Cấn, Đình Công Lê

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Abstract

Objective: to present clinical and laboratory findings of bilateral pheochromocytoma and laparoscopic bilateral adreclectomy results in children. Methods: a  case report. Results: a male - 14 years old accidentally was found of hypertension after traffic accident. Clinical examination revealed: no abdominal mass, no tenderness, hypercardia and hypertension. On abdominal ultrasound and CT scanner described bilateral adrenal mass (Right: 8cm, Left: 7cm). Laboratory findings showed that: total blood count and coagulation test is normal. HVA in urine was normal (2,34 micromol/l) and increased VMA in urine (18,58 micromol/l). The patient was diagnosed of biliateral pheochromocytoma pre-operatively. He was admiited at VN National Children’s Hospital to control blood pressure. After that, the management was the combination of L-adrenal artery blockage by stent and laparoscopic bilateral adrenalectomy. The patient’s condition after operation was stable. He was discharged after 10 days. The pathology result was bilateral pheochromcytoma without tumor on the borderline tissue. He was treated by hormone therapy and monitored carefully.  The patient has been followed up (3 months) until now with good result. Conclusion: Bilateral pheochromocytoma is a rare disease in children. The discussion between endocrinology doctor, anesthesis, surgeon and totally bilateral adrenalectomy show a good result.

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References

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