HEPATIC EPITHELIOID HEMANGIOENDOTHELIOMA: A RARE CASE REPORT

Anh Tú Đỗ , Hồng Thăng Vũ , Thị Hồng Nguyễn

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Abstract

Introduction: Epithelioid hemangioendothelioma (EHE) is a rare tumor of vascular origin. Hepatic epithelioid hemangioendothelioma (HEHE) is an extremely rare lesion, with an estimated incidence of only 1-2 cases in 1  milion people. Due to the diverse and rare clinical presentation, current treatment strategies in this patient group remain challenging for clinicians. Presentation of case: We report a 42-year-old female case with hepatic epithelioid hemangioendothelioma who was treated with AIM regimen chemotherapy at K hospital. Discussion: In this report, clinical features and optimal treament modalities for patient with hepatic epithelioid hemangioendothelioma are discussed. Conclusion: Hepatic epithelioid hemangioendothelioma is an extremely uncommon malignancy. Diagnosis is based on pathology results and immunohistochemical staining. Treatment strategies need to be individualized for each specific patient, with chemotherapy helping to alleviate symptoms and improve patient survival.

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References

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