COLONIC GIST IN CHILDREN: A CASE REPORT AND LITERATURE REVIEW

Nguyễn Thị Hồng Vân, Lương Anh Quân, Trần Văn Quyết, Trần Ngọc Sơn

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Abstract

Aim: Report a rare case of colonic GIST in a treatment child. Method: A case report and literature review. Result: A 13 years old girl was admitted to our center for abdominal pain, bilious vomiting and hematochezia. Abdomainal ultrasound showed a colon- colonic intussusception in the left lower quatdrant, 54 x 43 x 51mm in size. Computed tomography showed an intussuception with a lesion suspected for a left colonic tumor. Colonic endoscopy showed a decending colonic tumor with 40 x 30 mm in diameter with central necrosis. The patient underwent emergent laparoscopic reduction for the intussusception. On the first postoperative day, the patient suffered from recurrent intussusception with consequent intestinal obstruction. Segmental left colectomy was performed with the tumor margins 3-5 cm. The result of pathology showed GIST with microscopic free margins. The patient recovered well and was discharged on post operative day 7. At a follow up of 3 years, the patient had no complication, recurrence or metastasis. Conclusion: Colonic GIST is rare in children. Segmental colonic resection with negative margins can be curative for localized GIST.

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References

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