AMYLOIDOSIS WITH LIGHT CHAIN DEPOSITION CARDIOMYOPATHY: A CLINICAL CASE STUDY

Phi Hùng Trương

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Abstract

Light chain cardiac amyloidosis (AL-CA) is a disease caused by the accumulation of amyloid fibers in the heart muscle, formed due to the abnormal proliferation of plasma cells. This is one of the causes of heart failure, especially in heart failure with preserved ejection fraction, which clinicians need to identify and diagnose early because symptoms are nonspecific, and the prognosis is often poor if diagnosed late. We present a case of hospital admission for heart failure with preserved ejection fraction that exhibited several features suggestive of amyloidosis in clinical and imaging findings. The patient underwent additional tests to confirm the diagnosis and received initial in-hospital chemotherapy. This is a fairly typical case of light chain cardiac amyloidosis that we may encounter in clinical practice.

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References

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