PULMONARY ATRESIA WITH VENTRICULAR SEPTAL DEFECT: RESULTS OF TOTAL REPAIR SURGERY USING VALVED CONDUIT AT VIETNAM NATIONAL CHILDREN’S HOSPITAL

Quang Vịnh Trần, Hữu Nhật Nguyễn, Quốc Hưng Đoàn, Lý Thịnh Trường Nguyễn

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Abstract

Objectives: Describe the results of total repair surgery for pulmonary atresia with ventricular septal defect (PA/VSD) using valved conduit at Vietnam National Children's Hospital.Methods: This was a series case study. The study included all patients underwent total repair surgery for PA/VSD using valved conduit at Vietnam National Children's Hospital from January 2016 to December 2022. Results: 140 patients enrolled during the study period. There was 79 male patients (56%). At the time of surgery, the median age was 11.1 months, the median weight was 6.75 kg. The conduit Contegra (88%) and Hancock (12%) were implanted. Postoperative complications prolonged the duration of postoperative mechanical ventilation ≥ 68 h, and the ICU stay  ≥ 6 days (p < 0.01). The early mortality rate was 3.6%. The late mortality rate was 4.4%. The rate of re-operation and/or re-intervention was 21.6%. 127 patients completed the follow-up with a median of 3 years. The overall survival rate after a follow-up period of more than 5 years was 88.4%.Conclusions: The total repair surgery of PA/VSD using valved conduit at Vietnam National Children's Hospital resulted in good outcomes. Long-term study and monitoring of the progression of the pathology and assessment of the longevity of the artificial conduit are necessary

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References

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