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Date Published: 11/12/2023
Abstract Views: 400
Views PDF: 124
DOI: https://doi.org/10.51298/vmj.v532i2.7618
Issue
Vol. 532 No. 2 (2023)
Section
Các bài báo
How to Cite
Doãn, V. N., Mã, M. H., & Hoàng, Đình Âu. (2023). IMAGING FEATURES OF OHVIRA SYNDROME. Vietnam Medical Journal, 532(2). https://doi.org/10.51298/vmj.v532i2.7618

IMAGING FEATURES OF OHVIRA SYNDROME

Văn Ngọc Doãn1, Mai Hiền Mã2, Đình Âu Hoàng3,
1 University of Medicine and Pharmacy, Hanoi National University
2 HMU
3 Hanoi Medical University Hospital

Main Article Content

Abstract

OHVIRA syndrome, an acronym for « Obstructed Hemivagina Ipsilateral Renal Agenesis » was a rare anomaly of the urogenital system, usually diagnosed in infants, young children, and adolescent girls. OHVIRA syndrome was characterized by urogenital abnormalities such as didelphys uterus, duplication of the cervix and vagina, unilateral obstructed hemivagina, and ipsilateral renal agenesis. We reported a case that diagnosed with OHVIRA syndrome at Hanoi Medical University Hospital. A 10- year-old female patient with no menstrution yet was admitted to the hospital due to lower abdominal pain. Abdominal ultrasound and pelvic magnetic resonance imaging (MRI) showed a didelphys uterus consisting of two chambers, two cervixes, two vaginas, left-sided hydro/hematometrocolpos, and left kidney agenesis.

Article Details

Keywords

obstructed hemivagina, OHVIRA syndrome, renal agenesis, didelphys uterus

References

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