CASTLEMAN DISEASE: A CASE REPORT AND REVIEW OF THE LITERATURE

Thế Anh Phạm, Hoàng Quốc Đặng

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Abstract

Castleman disease is a rare lymphoproliferative disorder, first described by Benjamin Castleman in 19542. The disease has diverse clinical presentation and nonspecific pathological features that can be found in many diseases. Therefore, diagnosing this disease is difficult, especially preoperative diagnosis. Castleman disease can be divided into unicentric and multicentric types according to clinical presentation in one lymph node or multiple lymph nodes, or the hyaline vascular type and plasma cell type according to pathology. We present a 39-year-old female patient with a 2-day history of constant, dull, epigastric pain. Imaging studies revealed a mass in the head of the pancreas. The patient underwent a complete surgical resection of the tumor. Post-operatively, she recovered well without complications and was discharged after seven days of treatment.

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References

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